The 2025 complete neurology checklists updates

As we take stock of 2025…

Below is a reminder of how the year went at Neurochecklists.

 

22 NEW CHECKLISTS

 

Acute haemorrhagic leukoencephalitis (AHLE) 

Arterial tortuosity syndrome (ATS)

Benign paroxysmal torticollis (BPT)

CAPNON

Cerebral air embolism (CAE)

Cervical artery dissection (CAD): recurrence

Craniopharyngioma

Creutzfeldt Jakob disease (CJD) treatment

Cyclical vomiting syndrome

Deep gluteal syndrome (DGS)

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Developmental coordination disorder (DCD)

Dystypia and dystextia

Facet joint pain

Geschwind syndrome

Immune checkpoint inhibitor (ICI) paraneoplastic syndrome

Ischaemic stroke hand knob syndrome

KLHL11 paraneoplastic encephalitis

MOGHE

Senile dementia of the neurofibrillary tangle type (SDNFT)

Sinus pericrania

Strachan syndrome

Visual distortions

 

280 UPDATED CHECKLISTS

 

Aadrenoleukodystrophy (ALD): management

Aceruloplasminemia 

Agrypnia excitata

Agyrophilic brain disease clinical features

Alzheimer’s disease (AD) drug treatments 

Alzheimer’s disease (AD) risk factors

Alzheimer’s disease (AD): emerging investigations

Alzheimer’s disease (AD): protective factors

Alzheimer’s disease (AD): emerging investigations

Alzheimer’s disease (AD): investigational treatments

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Anti GFAP cytopathy: management

Anti glycine receptor syndrome: clinical features

Anti Ma2 encephalitis syndrome: clinical features

Anti-MAG neuropathy: clinical features

Anti-seizure medications: teratogenicity risk

Anti-synthetase syndrome

Antiphospholipid syndrome (APS) investigations 

 Antiplatelet therapy

Arachnoid cysts: clinical features

Arterial dolichoectasia: clinical features

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Ataxia telangiectasia (AT)

Atogepant

Autism: clinical features

Autism: management

Autoimmune encephalitis: clinical features

Autonomic dysfunction: investigations

Balint’s syndrome

Behavioural variant FTD: clinical features 

Behcet’s syndrome: management

Bell’s palsy: differentials 

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Biotidinase deficiency: clinical features

Bow hunters syndrome

Brachial neuritis: investigations

Brivaracetam

CAA-related inflammation (CAAri)

CASPR2 autoimmune encephalitis: management 

Cavernoma: treatment

Cavum septum pellucidum

Cerebral amyloid angiopathy (CAA) investigations

Cerebral amyloid angiopathy (CAA) radiological features

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Cerebral amyloid angiopathy (CAA) treatment 

Cerebral amyloid angiopathy (CAA): clinical features

Cerebral amyloid angiopathy (CAA): haemorrhage types

Cerebral aneurysms: clinical features

Cerebral aneurysms: risk factors

Cerebral vein thrombosis (CVT): clinical features

Cerebral vein thrombosis (CVT): risk factors

Cerebrotendinous xanthomatosis (CTX): management

Cervical artery dissection (CAD): risk factors

CGRP agonists

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CGRP monoclonal antibodies

Chanter syndrome

CIDP: clinical features

CIDP: immunosuppressant treatment 

CIDP: investigations

CJD: investigations

Clinically isolated syndrome (CIS): MS risk 

Cluster headache (CH): causes

Cluster headache (CH): clinical features

Cluster headache (CH): co-morbid disorders

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CMT type 4: genetic subtypes

CMT-X: genetic subtypes

Cns tuberculosis (TB) types

Corticobasal syndrome (CBS): clinical features

Covid 19: peripheral features

Covid 19 vaccine complications 

Cryopyrin associated periodic fever syndrome

Cultural startle syndromes

Deja vu

Dengue infection: neurological features

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Dengue infection: management 

Diabetic neuropathy: types

Distal hereditary motor neuropathy (dHMN): genetics

Down’s syndrome: neurological features

DPPX autoimmune encephalitis

Dravet syndrome: management

Drug-induced neuropathy

Drug-induced parkinsonism: risk factors

Duchenne muscular dystrophy (DMD): treatment

Dyskinesia: treatment

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Dystonia treatments

Embolic stroke of undetermined source (ESUS): management

Embolic stroke: treatment

Epicrania fugax

Epilepsy and autoimmune disorders

Epilepsy surgery

Epilepsy with eyelid myoclonia

Epilepsy: psychiatric manifestations

Epileptic encephalopathy: classification

Episodic ataxia type 2 (EA2) 

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Episodic ataxia: summary checklist

Erdheim Chester disease: clinical features

Familial amyloid neuropathy (FAP): treatment

Familial CJD

Familial partial epilepsy with variable foci 

FMTLE

Fragile x tremor ataxia syndrome (FXTAS): clinical features

Frontotemporal brain sagging syndrome (FBSS)

Frontotemporal dementia (FTD): clinical features 

Frontotemporal dementia (FTD): differential diagnosis

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Frontotemporal dementia (FTD): management

FSHD: variant phenotypes

Functional cognitive disorder

Functional seizures: risk factors

Functional seizures: complications

Functional tremor

GAD antibody phenotypes

Gene-specific epileptic encephalopathy: classification

GFAP encephalitis: clinical features

GFAP encephalitis: management

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Giant cell arteritis (GCA): treatment 

Giant tumefactive perivascular spaces

Gordon Holmes syndrome (GHS)

Guillain barre syndrome (GBS): prognosis

Haematoma expansion

Hemicrania continua: causes

Hepatitis B virus (HBV) neurology

Huntington’s disease (HD): clinical features

Huntington’s disease (HD): treatment

Hypertrophic pachymeningitis: causes

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Hypothalamic hamartoma: management

Idiopathic hypersomnia management

Idiopathic intracranial hypertension (IIH) clinical features

Idiopathic intracranial hypertension (IIH): dural venous sinus stenting

IgLON5 antibody disease: clinical features 

IgLON5 antibody disease: management

Immune checkpoint inhibitor (ICI) myopathy

Immune mediated necrotizing myopathy (IMNM): causes

Inclusion body myositis (IBM): clinical features 

Intra-arterial dolichoectasia features 

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Intracerebral haemorrhage (ICH): risk factors

Intracerebral haemorrhage (ICH): causes

Intracranial dural AV fistula (AVF)

LARS2 leukoencephalopathy

Laryngeal dystonia

Limbic predominant age-related tdp43 encephalopathy (LATE)

Low pressure hydrocephalus

Lumbar puncture (LP): complications 

Lumbosacral plexopathy: causes

Lyme neuroborreliosis: clinical features

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Malformations of cortical development (MCD): other genes

Metachromatic leukodystrophy (MLD)

Migraine: acute treatment

Migraine: evidenced preventative options

Mirror movements

Mitochondrial POLG disorders: management

MOG antibody disease (MOGAD: outcome

MOG antibody disease (MOGAD): MRI features

Molybdenum cofactor deficiency: management

Motor neurone disease (MND): prognosis 

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Motor neurone disease (MND): protective factors

Motor neurone disease (MND): clinical features

Motor neurone disease (MND): differential diagnosis

Motor neurone disease (MND): investigational drug treatments

Motor neurone disease (MND): minor genetic risk factors

Motor neurone disease (MND): non-genetic risk factors

Motor neurone disease (MND): non-invasive ventilation

Motor neurone disease (MND): other genetic risk factors

Motor predominant neuropathy

Moyamoya disease: clinical features

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Multifocal motor neuropathy (MMN): clinical features

Multiple sclerosis (MS) and seizures

Multiple sclerosis (MS): breastfeeding

Multiple sclerosis (MS): clinical features

Multiple sclerosis (MS): CSF analysis

Multiple sclerosis (MS): investigational treatments

Multiple sclerosis (MS): modifiable risk factors

Multiple sclerosis (MS): MRI features

Multiple sclerosis (MS): neurological features

Multiple sclerosis (MS): poor prognostic factors

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Multiple sclerosis (MS): protective factors

Multiple system atrophy (MSA) clinical features

Multiple system atrophy (MSA) investigations 

Multisystem proteinopathy: investigations

Musk myastheni gravis (MG): management

Musk myasthenia gravis (MG): management 

Myasthenia gravis (MG): AChR antibody

Myasthenia gravis (MG): clinical features 

Myasthenia gravis (MG): investigational treatments 

Myasthenia gravis (MG): non-immunosuppression agents

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Myasthenia gravis (MG): immunosuppression treatment

Myasthenia gravis (MG): triggers

Myasthenic crisis: risk factors 

Myotonic dystrophy and cancer

Myotonic dystrophy type 1: neurological features

Myotonic dystrophy: clinical features

NAION: clinical features 

Narcolepsy: secondary causes

Natalizumab

Nemaline myopathy: genetics

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Neoplastic meningitis: investigations

Neuroangiostrongyliasis: management

Neurocysticercosis: pathology

Neurological guidelines directory

Neurolymphomatosis 

Neuromyelitis optica (NMO): clinical differentials 

Neuromyelitis optica (NMO): CSF analysis 

Neuromyelitis optica (NMO): MRI features

Neuromyelitis optica (NMO): treatment

Neurosarcoidosis: CSF analysis

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Neurosarcoidosis: investigations

Neurosarcoidosis: cranial features

Neurosyphilis: management

Niemann-Pick C disease: treatment

NMDAR encephalitis: atypical features

NMDAR encephalitis: investigations

NMDAR encephalitis: treatment

NMDAR encephalitis: clinical features

Nodding syndrome: clinical features

Non-compressive myelopathy

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Non-convulsive status epilepticus (NCSE): clinical features

Normal pressure hydrocephalus (NPH): clinical features

Ocrelizumab

Palatal tremor

PANDAS

Parkinsn’s disease (PD): investigational treatments

Parkinsn’s disease (PD): premotor features

Parkinson’s disease (PD) investigations 

Parkinson’s disease (PD) neurological risk factors 

Parkinson’s disease (PD): differential diagnosis

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Parkinson’s disease (PD): genetic classification

Parkinson’s disease (PD): protective factors

Parkinson’s disease (PD): systemic features

Parkinson’s disease (PD): systemic risk factors

Paroxysmal kinesigenic dyskinesia (PKD) clinical features 

Pembrolizumab toxicity

Post stroke seizures

Primary angiitis of the cns (PACNS) investigations 

Primary lateral sclerosis (PLS) clinical features 

Primary progressive aphasia non-fluent variant (NFVPPA)

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Progressive multifocal leukoencephalopathy (PML): investigations

Progressive supranuclear palsy (PSP) clinical features

Progressive supranuclear palsy (PSP) differential diagnosis 

Progressive supranuclear palsy (PSP): clinical features

Rabies: treatment 

Rasmussen’s encephalopathy (RE): management

Reflex seizures

Refractory epilepsy: drug treatments

Refractory epilepsy: interventional treatments

Refractory status epilepticus: treatment

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Restless legs syndrome (RLS): clinical features

Rituximab

ROHHAD: management

Rosai dorfman disease (RDD): differential diagnosis

Ruptured arachnoid cysts

Schistosomal meloradiculopathy

Schizophrenia: treatment

Seizure manifestations 

Seizures: neurological features

Sickle cell disease: neurological features

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Sickle cell disease: treatments

Siponimod

SLIPPERS

Smart syndrome: management

Snake bite toxicity: clinical features

Spastic paraparesis: causes

Spinocerebellar ataxia 27 (SCA 27)

Spinocerebellar ataxia 3 (SCA 3): clinical features

Spontaneous intracranial hypotension (SIH) clinical features

Spontaneous intracranial hypotension (SIH): treatment

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SSPE: clinical features 

Stiff person syndrome (SPS): investigational treatments

Stiff person syndrome (SPS): treatments

Stroke: investigational drugs

Stroke: secondary prevention

Stroke: thrombolysis agents

Subarachnoid haemorrhage (SAH): complications

SUDEP: clinical indicators

SUNCT: treatment

Synaesthesia clinical features

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Systemic seizures: manifestations

Transverse myelitis (TM)

Traumatic brain injury (TBI): complications

Tremors: medical causes

Trigeminal neuralgia (TN): clinical features

Triptans: adverse effects

Triptans: clinical use

TTR amyloidosis neuropathy: treatment

Tumefactive demyelination: causes

Tumefactive MS: differential diagnosis

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Uraemic encephalopathy

Vagus nerve stimulation (VNS)

Valproate: adverse effects

Vein of Galen aneurysmal malformation (VGAM)

Viral encephalitis: management

West nile virus (WNV) infection: management

Wilson’s disease: MRI features

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